|
KMID : 0191119980130050548
|
|
Journal of Korean Medical Science
1998 Volume.13 No. 5 p.548 ~ p.550
|
|
|
Acute hemolytic crisis with fulminant hepatic failure as the first manifestation of Wilson´s disease: a case report
|
|
Lee JJ
Kim HJ/Chung IJ/Kook H/Byun JR/Kwon SY/Park MR/Choi KS/Hwang TJ/Ryang DW
|
|
|
Abstract
|
|
|
|
We report a 27-year-old woman who developed Coombs' negative hemolytic anemia and fulminant hepatic failure as the initial manifestation of Wilson's disease. Unmeasurably low level of serum alkaline phosphatase provided a clue to the diagnosis of Wilson's disease. The diagnosis was established with the presence of Kayser-Fleischer ring, decreased serum ceruloplasmin level, and elevated urine and serum copper levels. In spite of repeated plasmapheresis, she died of multiorgan failure on the fifth hospital day.
|
|
|
KEYWORD
|
|
|
|
|
|
FullTexts / Linksout information
|
|
 
|
|
|
Listed journal information
|
|
    
|